Facioscapulohumeral Muscular Dystrophy G71.11 359.0

  synonyms: FSHD
Facioscapulohumeral Muscular Dystrophy ICD-10

Facioscapulohumeral Muscular Dystrophy ICD-9

  • 359.0 Congenital hereditary muscular dystrophy

Facioscapulohumeral Muscular Dystrophy 

  • Autosomal dominant transmition, wide range of expression
  • Often characterized by weakness and impaired shoulder funtion. Muscle involvement is diffuse, but the deltoid muscle is usually spared.
  • Scapular winging often results. Scapulathoracic fusion improves upper extremity function.
  • Atasoy E, JBJS 2000;82Br;813
  • Bunch WH, JBJS 1993;75A;372