Polydactyly
synonyms:
Polydactyly ICD-9
Polydactyly Etiology / Epidemiology / Natural History
- Prexial polydactyly = thumb polydactyly
- Males > females
- Causcasion > African American
- Sporadic
- Postaxial polydactyly = duplication of the ulnar most digit
-Autosomal dominant inheritance
-Blacks > whites
-Generally isolated condition in blacks, ossociated with other organ system dysfunction in whites.
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Polydactyly Anatomy
Polydactyly Clinical Evaluation
Polydactyly Xray / Diagnositc Tests
Polydactyly Classification / Treatment
- Wassel Classification (Wassel HD, CORR 1969;64:175).
- Wassel Type I: bifid distal phalanx
- Wassel Type II: duplicated distal phalanx
- Wassel Type III: bifid proximal phalanx
- Wassel Type IV: duplicated proximal phalanx
- Wassel Type V: bifid metacarpal
- Wassel Type VI: duplicated metacarpal
- Wassel Type VII: thumb polydactyle with associated triphangeal thumb
- Treatment: ablation of the radial thumb with radial collateral ligament reconstruction and advancement of the thenar insertions to the retained ulnar thumb. +/- corrective osteotomies as indicated.
- Postaxial
-Type A(fully developed): ecsion with collateral ligament and hypothenar muscle reconstruction.
-Type B (rudim entary and pedunculated): consider suture ligation in newborn nursery
Polydactyly Associated Injuries / Differential Diagnosis
- Associated congenital anomalies are rare
Polydactyly Complications
Polydactyly Follow-up Care
Polydactyly Review References
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